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Updated: Jun 21, 2025

Utility of Dissociated Intrinsic Hand Muscle Atrophy in the Diagnosis of Amyotrophic Lateral Sclerosis
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骨肌参与全身性氨基粉症往往被忽视

Jingwen Xu1,2, Xiaoyu Zhou1, Yingxin Wang1

  • 1Research Institute of Neuromuscular and Neurodegenerative Diseases, Qilu Hospital, Cheeloo College of Medicine, Shandong University, Jinan, China.

Neuropathology and applied neurobiology
|July 10, 2024
PubMed
概括

系统性amyloidosis经常涉及骨肌肉,但症状性肌肉病变很少见. 这项研究在大多数患者中发现了粉样蛋白沉积,但只有少数患有肌肉衰弱,这表明无症状肌肉参与的诊断不足.

关键词:
氨基化物 氨基化物轻链氨基粉症的发生这是骨肌肉的骨架肌肉.转胺氨基化症的发生.

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