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Updated: Jul 30, 2026

Imaging Features of Systemic Sclerosis-Associated Interstitial Lung Disease
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病例报告:常见的可变免疫缺陷表型和粒状淋巴细胞间歇性肺病与新型SOCS1变异

María Soledad Caldirola1,2, Espantoso Daiana1, Andrea Cecilia Gomez Raccio1

  • 1Servicio de Inmunología, Hospital de Niños "Dr. Ricardo Gutiérrez", Buenos Aires, Argentina.

Frontiers in pediatrics
|July 15, 2024
PubMed
概括

常见变性免疫缺陷 (CVID) 患者可能会患上严重的肺部疾病. 这项研究详细介绍了阿根廷首位患有CVID和与SOCS1基因变异相关的粒状淋巴细胞间歇性肺病的患者.

关键词:
格利尔德 (GLILD) 的意思是在SOCS1中,SOCS1是SOCS1.常见的可变免疫缺陷常见的免疫缺陷.粒状淋巴细胞间歇性肺部疾病免疫的先天错误 免疫的先天错误

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