没有MAPCA的PA-VSD:长期结果和重新干预的审查
Elizabeth H Stephens1, Joseph A Dearani1, William R Miranda2
1Department of Cardiovascular Surgery, Mayo Clinic, Rochester, MN, USA.
World journal for pediatric & congenital heart surgery
|July 23, 2024
概括
肺动脉缩的长期存活率与心室隔膜缺陷没有主要的肺动脉附带动脉是大约80%在十年. 完整的修复和充足的肺动脉改善了结果,尽管重新干预是常见的.
科学领域:
- 心脏病学 心脏病学
- 儿童心脏病学 儿童心脏病学
- 遗传性心脏病是一种先天性心脏病.
背景情况:
- 肺动脉缩与心室隔膜缺陷 (VSD) 没有主要的肺上侧动脉 (MAPCAs) 是一种罕见的先天性心脏缺陷.
- 随着先天性心脏病的生存率的提高,我们需要了解这一特定人群的长期结果.
研究的目的:
- 审查VSD但没有MAPCAs的肺动脉缩患者的长期结果和结局.
主要方法:
- 对PubMed数据库进行了全面的文献审查.
- 包括从1990年到现在以英语出版的研究,重点关注肺动脉缩,VSD和右心室-肺动脉等关键词.
- 分析包括检查整体队列,特别是对没有MAPCA的患者进行亚组分析.
主要成果:
- 十年后的生存率接近80%,受到完全修复和更大的肺动脉的积极影响.
- 不完全的修复与较差的生存结果有关.
- 患者经常需要对右心室外流通道进行重复干预,而肺动脉的低可塑性是重复干预的危险因素.
结论:
- 没有MAPCA的VSD肺动脉缩的长期结果有所改善.
- 完整的手术修复和发达的肺动脉对于有利的生存至关重要.
- 重新干预,无论是手术还是以导管为基础的,都是常见的长期后果,主要涉及右心室外流通道.
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