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Updated: Jun 18, 2025

Phosphorus-31 Magnetic Resonance Spectroscopy: A Tool for Measuring In Vivo Mitochondrial Oxidative Phosphorylation Capacity in Human Skeletal Muscle
09:40

Phosphorus-31 Magnetic Resonance Spectroscopy: A Tool for Measuring In Vivo Mitochondrial Oxidative Phosphorylation Capacity in Human Skeletal Muscle

Published on: January 19, 2017

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线粒体生物能学和心脏脂蛋白重塑线粒体三功能蛋白质缺乏症异常中的异常

Eduardo Vieira Neto1,2, Meicheng Wang1, Austin J Szuminsky3

  • 1Genetic and Genomic Medicine Division, Department of Pediatrics, UPMC Children's Hospital of Pittsburgh.

JCI insight
|August 1, 2024
PubMed
概括

线粒体三功能蛋白 (TFP) 缺乏影响脂肪酸氧化和心脏脂蛋白重塑. 患者细胞表现出多样化的生物能量反应,尽管普遍降低了心脏脂蛋白,这表明药物有效性取决于基因型.

关键词:
脂肪酸氧化过程中的脂肪酸氧化.遗传学 是一个遗传学.中间代谢是代谢的中间体.代谢过程中的代谢.线粒体中的线粒体.

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Analyzing Oxygen Consumption Rate in Primary Cultured Mouse Neonatal Cardiomyocytes Using an Extracellular Flux Analyzer11:26

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