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Leonardo Oliveira Mendonça1, Marie-Louise Frémond2

  • 1Division of Clinical Immunology and Allergy, School of Medicine, University of São Paulo, São Paulo, Brazil; Discipline of Clinical Immunology and Allergy, Department of Internal Medicine, Universidade de Santo Amaro (UNISA), São Paulo, Brazil.

概括

异常的I型干扰素分泌会导致干扰素病变,这是一组自身炎症性疾病. 本综述涵盖了他们的免疫遗传学,诊断和治疗,包括艾卡迪-古蒂耶综合征和系统性红斑狼.