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Updated: Jun 17, 2025

Visualization of Mitochondrial Respiratory Function using Cytochrome C Oxidase / Succinate Dehydrogenase COX/SDH Double-labeling Histochemistry
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在遗传性和获得性肌肉疾病的范围内的二次线粒体功能障碍

Gloria Mak1, Mark Tarnopolsky2, Jian-Qiang Lu3

  • 1University of Alberta, Department of Neurology, Edmonton, Alberta, Canada.

Mitochondrion
|August 12, 2024
PubMed
概括

骨肌的线粒体是动态网络,对能量生产至关重要. 这篇评论探讨了各种肌肉病的线粒体功能障碍,讨论了原因和潜在的治疗方法.

关键词:
生产性肌肉病变是一种先天性肌肉病变.炎症性肌肉病变是一种炎症性肌肉病变.线粒体功能障碍 线粒体功能障碍肌肉发育不良症 肌肉发育不良

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