双边水平通道发育不良表现为听力损失与复发性,模仿Meniere的疾病
Wonyong Baek1, Young Jae Lee1, Gi-Sung Nam1
1Department of Otorhinolaryngology-Head and Neck Surgery, Chosun University College of Medicine, Gwangju, South Korea.
Ear, nose, & throat journal
|August 29, 2024
概括
这项研究详细介绍了一种罕见的双边水平半圆通道 (HSC) 发育不良症,导致听力损失和. 这种情况模仿了Meniere.
科学领域:
- 耳鼻喉科 耳鼻喉科 耳鼻喉科
- 神经科学是一个神经科学.
- 发展生物学 发展生物学
背景情况:
- 水平半圆通道 (HSC) 形是骨迷宫的罕见发育异常.
- 这些异常可以呈现出不同程度的听力损失和前庭功能障碍.
- 双边的HSC发育不良是非常罕见的.
研究的目的:
- 报告一种极为罕见的双边水平半圆通道 (HSC) 发育不良的病例.
- 描述这种疾病的临床表现,诊断结果和潜在的病理生理学.
- 为了突出显示HSC发育不良和Meniere病之间的差异诊断.
主要方法:
- 一个49岁的男性患者的病例报告,他有3年的复发性和听力损失病史.
- 听力学评估包括纯音调听力测量.
- 静脉功能测试,包括双热热量测试.
- 骨的高分辨率计算机断层扫描 (CT).
主要成果:
- 患者出现了反复出现的头和左侧听力损失,模仿梅尼尔氏病.
- 听力测量显示左耳轻度至中度低频听力损失.
- 热量测试显示左侧通道;其他前庭检测正常.
- CT成像证实了双边HSC发育不良,其特征是低发育,融合的骨岛屿和左侧扩大的前庭.
结论:
- 双边水平半圆通道 (HSC) 形是一种极其罕见的疾病.
- 这种异常可以表现为模仿梅尼尔病的症状,包括和听力损失.
- 由于HSC发育不良而导致的内淋巴体水可能是观察到的症状的根本原因.
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