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Updated: Jun 14, 2025

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在Desminopathy和Titinopathy中的常见和关键差异性致病途径

Qiuxiang Li1,2, Liqun Xu1,2, Huiqian Duan1,2

  • 1Department of Neurology, Xiangya Hospital, Central South University, Changsha, China.

International journal of medical sciences
|September 6, 2024
PubMed
概括

肌纤维肌病 (MFM) 涉及到条纹肌肉损伤. 蛋白质组学揭示了MFM常见的细胞骨失调和线粒体问题,在desminopathy和titinopathy中具有明显的糖解和细胞外矩阵变化.

关键词:
细胞骨架 细胞骨架脱敏症 (desminopathy) 是一种脱敏症.葡萄糖溶解是什么肌纤维纤维肌肉病变 (myofibrillar myopathy) 是一种神经纤维纤维肌肉病变.蛋白质组学 蛋白质组学标病变 - 标病变是一种病变.

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