巨大的瘤形成性半脑脑体维尔霍 - 罗宾空间与三腔体脑症:一个基于案例的系统文献综述
Sivaraman Kumarasamy1,2, Pietro Spennato1, Giuliana Di Martino1
1Department of Neurosciences, Pediatric Neurosurgery Unit, Santobono-Pausilipon Children's Hospital (AORN) , Via Mario Fiore n. 6, 80129, Naples, Italy.
概括
儿童大脑干中巨大的扩张维尔霍-罗宾空间 (VRSs) 是罕见的,可以导致阻塞性水脑. 手术性囊窗通过解决水脑和质量效应,提供了立即的症状缓解.
科学领域:
- 神经科学是一个神经科学.
- 神经外科 神经外科
- 儿科神经学 儿科神经学
背景情况:
- 周血管空间,也称为Virchow-Robin空间 (VRSs),可以在脑干中扩张.
- 大脑干中扩展的VRS是罕见的,通常会导致阻塞性水脑或对神经结构的质量影响.
研究的目的:
- 在儿童中呈现巨型瘤性VRS与水头的病例.
- 审查文献并评估这种罕见疾病的治疗选择.
主要方法:
- 治疗了一名患有巨型瘤性大脑半球体VRS和水脑的儿科患者.
- 治疗涉及内镜第三室内静脉切除术,随后进行多次显微镜和内镜囊.
- 文献审查确定了12个案例,包括索引案例,以分析治疗结果.
主要成果:
- 该患者出现了头痛,并被诊断出患有巨型瘤性半脑体VRS,导致三室水脑.
- 初始治疗以内镜第三腔静脉切除术和囊窗化,随后由于囊再生而重复进行多次窗化.
- 文献审查表明,在报告的病例中,41.7%的病例中进行了囊化 (内镜或显微镜).
结论:
- 巨型大脑半脑体扩张VRS在儿童中不常见,通常存在阻塞性水脑.
- 外科干预包括内镜第三腹腔静脉切除术,腹腔静脉切除术或直接囊透膜术.
- 囊窗可以立即缓解症状,但由于疾病进展的风险,密切跟踪是必不可少的.
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