患有IPEX综合征的患者的不同临床和免疫学特征:来自土耳其的多中心分析

Hayrunnisa Bekis Bozkurt1, Feyza Bayram Catak2,3,4, Ali Sahin5

  • 1Faculty of Medicine, Department of Pediatric Allergy and Immunology, Istanbul Medeniyet University, Istanbul, Turkey.

PubMed
概括

IPEX综合征是一种罕见的自身免疫性疾病,表现出多种不同的症状. 造血干细胞移植 (HSCT) 提供了持续的控制,而西洛在IPEX患者的免疫抑制剂中显示出有前途.

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