儿童脏失生症的特点 儿童脏失生症的特点
Ece Mekik1, Zeynep Birsin Özçakar1, Nilgun Cakar1
1Pediatric Nephrology, Ankara University School of Medicine, Ankara, Turkey.
Klinische Padiatrie
|September 20, 2024
概括
功能障碍 (RD) 亚型在儿童中表现出明显的特征和预后. 个性化随访至关重要,专注于蛋白尿和高血压等并发症,以获得儿童病的更好的结果.
科学领域:
- 儿科脏病学 儿科脏病学
- 泌尿器科 泌尿器科 泌尿器科 泌尿器科
- 遗传学 遗传学 是一个
背景情况:
- 功能障碍 (RD) 是儿童慢性病 (CKD) 的主要原因.
- 本研究详细介绍了各种RD亚型的独特特征.
研究的目的:
- 在儿科患者中分析不同功能障碍亚型的不同临床和预后特征.
- 为了告知个性化的患者治疗策略,功能障碍.
主要方法:
- 从2018年1月到2019年6月,对198名患有RD的儿童进行了横截面研究.
- 将其分为单边的RD,双边的RD,后部尿道 (PUV) 和多囊性 - 失塑性脏 (MCDK).
主要成果:
- 血缘关系总体为22%,在双边研发和开发中增加到56%.
- 高血压 (16%) 和蛋白尿 (20%) 在双边RD和PUV组中更为普遍.
- 23%的患者患有CKD,双边RD和PUV的发病率更高;12名患者接受了移植.
结论:
- RD亚型表现出独特的临床和预后特征.
- 对于儿科RD患者来说,个性化的随访是必不可少的.
- 建议密切监测可修改的并发症,如蛋白尿和高血压.
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