在囊性纤维化中挑战的尿液二碳酸盐分泌试验:尿酸/基参数的全面分析

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Updated: Jun 12, 2025

Real-Time, Semi-Automated Fluorescent Measurement of the Airway Surface Liquid pH of Primary Human Airway Epithelial Cells
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Amalie Q Rousing1, Majbritt Jeppesen2, Søren Jensen-Fangel2

  • 1Department of Biomedicine, Aarhus University, Aarhus, Denmark.

Acta physiologica (Oxford, England)
|September 23, 2024
PubMed
概括

挑战性尿液二碳酸盐 (HCO3-) 测试有效地评估囊性纤维化转膜导电性调节器 (CFTR) 在患有囊性纤维化 (pwCF) 患者中的功能. 这项测试显示pwCF中脏酸分泌受损,CFTR调节器治疗改善.

关键词:
在CFTR中,CFTR是最重要的.酸/是指一种酸/.碳酸二氧化碳的使用方法囊性纤维化症是什么脏 脏 脏是什么?

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