总异常的肺静脉连接与罕见的直接右心室排水和前所未有的配列共存的多系统变异
Arun Sharma1, Dollphy Garg1, Shivali Arya1
1Department of Radiodiagnosis, Postgraduate Institute of Medical Education and Research, Chandigarh, India.
这项研究报告了一种罕见的全异常肺静脉连接 (TAPVC) 病例,肺静脉在没有异构的情况下直接流入右心室. 该患者还呈现出独特的肺,血管和骨异常共存.
科学领域:
- 心脏病学 心脏病学
- 儿童心脏病学 儿童心脏病学
- 医疗成像医学成像
背景情况:
- 总异常肺静脉连接 (TAPVC) 涉及肺静脉异常排水进入全身循环.
- 心内TAPVC通常通过冠状动脉鼻排水到右心室.
- 与右心房直接的肺静脉连接是罕见的,通常与右心房异构有关.
研究的目的:
- 在儿童中呈现TAPVC与直接右心房排水的独特病例.
- 为了突出罕见相关异常的同时发生.
- 为了对罕见的先天性心脏缺陷的文献做出贡献.
主要方法:
- 一个10岁男孩的案例报告.
- 使用计算机断层扫描 (CT) 图像进行诊断评估.
- 详细分析心脏,肺,血管和骨结构.
主要成果:
- 一名10岁的男性接受了TAPVC,其特点是肺静脉直接流入右心室,没有冠状动脉鼻参与或右心室异构.
- CT成像显示了共存的异常:没有右肺肺裂,左环流动脉弧与牛分支,双侧宫肋骨和C7脊椎融合.
- 这种特殊的异常组合在文献中是前所未有的.
结论:
- 这种病例代表了一种罕见的TAPVC变体,具有独特的排水模式.
- 与这种TAPVC变种同时出现多种罕见的肺,血管和骨异常是非常不寻常的.
- 这份报告强调了全面成像在诊断复杂的先天性心脏病和相关异常时的重要性.
更多相关视频
06:48Three-Dimensional Echocardiographic Method for the Visualization and Assessment of Specific Parameters of the Pulmonary Veins
Published on: October 28, 2020
13:10Direct Re-implantation of Left Coronary Artery into the Aorta in Adults with Anomalous Origin of Left Coronary Artery from the Pulmonary Artery ALCAPA
Published on: April 24, 2017
相关概念视频
Overview of Systemic Veins
The coronary sinus, the heart's principal vein, resides in the coronary sulcus on the heart's posterior aspect. This broad venous channel receives nearly all venous blood from the myocardium, the heart muscle. It is fed by three primary veins: the great cardiac vein, the...
Coronary Circulation
Coronary circulation begins at the base of the aorta, where two main arteries arise—the left and right coronary arteries. These arteries encircle the heart in the coronary sulcus and supply the...
Veins of Thorax
The azygos vein, positioned just right of the midline and anterior to the vertebral column, begins at the junction of the right ascending lumbar and subcostal veins, terminating in the superior vena cava. This vein drains blood from the right side of the thoracic wall, thoracic viscera, and posterior abdominal wall.
The...
Overview of Systemic and Pulmonary Circulation
The oxygenated blood is sent...
Cardiovascular System Abnormal Findings II: Auscultation
Abnormal Heart Sounds
Gallops:
Fetal Circulation
Two umbilical arteries transport blood from the fetus to the placenta. At the placenta, the blood absorbs oxygen and nutrients while simultaneously eliminating waste products. This oxygen-enriched and nutrient-rich blood then returns to the fetus through one...
