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儿科炎症性脑白细胞病变 儿科炎症性脑白细胞病变

Omar Abdel-Mannan1, Yael Hacohen1

  • 1Department of Neuroinflammation, Queen Square MS Centre, UCL Queen Square Institute of Neurology, Faculty of Brain Sciences, University College London, London, United Kingdom; Department of Neurology, Great Ormond Street Hospital, London, United Kingdom.

Handbook of clinical neurology
|September 25, 2024
PubMed
概括

在儿童中获得的脱髓化综合征 (ADS),包括多发性硬化症 (MS),与髓寡基细胞蛋白抗体相关疾病 (MOGAD) 和水素4抗体阳性神经髓炎光学谱系障碍 (AQP4-NMOSD) 不同. 区分这些疾病对于有效的治疗策略至关重要.

关键词:
在水-4抗体.改变疾病的疗法.模仿者 模仿者 模仿者髓寡腺细胞糖蛋白抗体与相关疾病相关的抗体.视觉神经炎光学谱系障碍儿科多发性硬化症儿童多发性硬化症

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科学领域:

  • 儿科神经学 儿科神经学
  • 神经免疫学 神经免疫学
  • 脱线性疾病 脱线性疾病

背景情况:

  • 获得性脱髓化综合征 (ADS) 是影响儿童视神经,大脑或脊髓的急性神经疾病.
  • 虽然多发性硬化症 (MS) 是一种常见的ADS复发性形式,但已经确定了其他不同的实体,如髓寡干细胞蛋白抗体相关疾病 (MOGAD) 和水素4抗体阳性神经omyelitis光谱障碍 (AQP4-NMOSD).
  • 历史上被认为是MS的变体,MOGAD和AQP4-NMOSD现在根据累积证据被认为是单独的疾病.

研究的目的:

  • 在儿科患者中划分获得性脱髓化综合征 (ADS) 的不同亚型.
  • 为了突出多发性硬化症 (MS),MOGAD和AQP4-NMOSD之间的差异,尽管临床重叠.
  • 强调准确诊断对于指导儿童ADS治疗的重要性.

主要方法:

  • 对临床,生物和病理学证据的审查,区分MS,MOGAD和AQP4-NMOSD.
  • 对儿科ADS诊断标准和表型特征的分析.
  • 对这些不同疾病的当前和新兴治疗方法的检查.

主要成果:

  • 生物学,临床和病理学数据证实MOGAD和AQP4-NMOSD是MS不同的实体.
  • 现型重叠存在,但并不排除MS,MOGAD和AQP4-NMOSD之间的差异化.
  • 许多炎症和非炎症性疾病可以模仿儿童的ADS,需要仔细诊断.

结论:

  • 准确地区分儿科MS,MOGAD和AQP4-NMOSD对于适当的患者管理至关重要.
  • 对于MS的疾病修饰疗法的进展以及对MOGAD和AQP4-NMOSD的新兴治疗方法强调了对精确诊断的需求.
  • 识别ADS的模仿者对于在儿科神经保健中有效的治疗计划至关重要.