GATA2,BAFF

Motoko Yasutomi-Sakai1, Taihei Hayashi1, Koji Suzuki1

  • 1Department of Pediatrics, Faculty of Medical Sciences, University of Fukui, Fukui, Japan.

概括

缺乏GATA2可以导致对类固醇有反应的肺部疾病,即使单细胞数量低. 这表明一种类似于联合可变免疫缺陷肺病的机制,涉及B细胞问题和自身免疫力.