一个患有赫曼斯基-普德拉克综合征的患者的急性视角关闭玻璃眼病发作:一个病例报告
Sebastián J Vázquez-Folch1, Gabriel A Jiménez-Berríos1, Natalio Izquierdo2
1School of Medicine, Universidad Central del Caribe, Bayamón, PRI.
Cureus
|October 7, 2024
概括
赫曼斯基-普德拉克综合征 (HPS) 类型1可能导致白内障手术后的急性角度闭眼光. 快速的YAG激光 iridotomy 有效降低眼内压力并使患者稳定.
科学领域:
- 眼科医生 眼科 眼科
- 遗传学 是一个遗传学.
- 内部医学 内部医学
背景情况:
- 赫曼斯基-普德拉克综合征 (HPS) 是一种罕见的遗传疾病.
- HPS的特点是眼皮白化,出血问题和状体沉积.
- 并发症包括肺纤维化和结肠炎.
研究的目的:
- 在患有HPS型1的患者中报告急性角闭光眼的病例.
- 描述白内障手术后这种并发症的管理.
主要方法:
- 一名63岁的女性患有1型HPS,接受了白内障手术.
- 由于瞳孔阻塞,她患上了急性闭角玻璃眼.
- 在手术前服用氨基酸后,治疗涉及YAG激光 iridotomy.
主要成果:
- 患者呈现出严重的眼睛疼痛和眼内压力升高.
- YAG激光虹膜切除术成功地缓解了瞳孔堵塞.
- 眼内压力显著下降,患者的病情稳定.
结论:
- 急性角闭光眼是接受白内障手术的HPS患者的潜在并发症.
- 及时干预YAG激光 iridotomy是有效的管理这种情况.
- 精心的手术前规划对于管理HPS患者出血风险至关重要.
相关概念视频
Angle Closure Glaucoma: Treatment
448
Angle-closure glaucoma, or closed-angle glaucoma, is an eye condition where the iris bulges out and blocks the iridocorneal angle, resulting in a buildup of aqueous humor and increased intraocular pressure. Immediate medical attention is necessary due to the sudden onset of symptoms. The treatment for angle-closure glaucoma includes short-term and long-term approaches. Short-term treatment involves using eye drops like pilocarpine to lower intraocular pressure by increasing aqueous humor...
448
Glaucoma: Overview
527
Glaucoma is an eye condition characterized by increased intraocular pressure that damages the retina and optic nerve, leading to irreversible blindness if left untreated. The human eye has various components, including the cornea, iris, pupil, lens, and optic nerve. Aqueous humor is secreted by the epithelium of the ciliary body in the posterior chamber and flows through the trabecular meshwork and canal of Schlemm, maintaining normal intraocular pressure. The trabecular meshwork and the canal...
527
Open Angle Glaucoma: Treatment
403
In open-angle glaucoma, the iridocorneal angle remains open, but the trabecular meshwork becomes stiff, slowing down the outflow of aqueous humor. This causes a buildup of aqueous humor in the anterior chamber, leading to a sudden increase in intraocular pressure. The treatment for open-angle glaucoma focuses on reducing the elevated intraocular pressure by either decreasing the secretion of aqueous humor or increasing its outflow.
Drugs such as carbonic anhydrase inhibitors, α2- and...
Drugs such as carbonic anhydrase inhibitors, α2- and...
403


