在苏萨克综合征中表现出前庭耳表现的表现:一个队列研究
Astrid Roelens1, Maria Vandekerckhove2, Leen Maes3
1Department of Otorhinolaryngology, Department of Head and Skin, Ghent University Hospital, Ghent, Belgium. astrid.roelens@ugent.be.
概括
在苏萨克综合征 (SuS) 中,静脉腔干扰是常见的. 在SUS患者中,早期的,积极的免疫抑制可以预防严重的听力损失和内耳功能障碍.
科学领域:
- 神经学 神经学
- 眼科医生 眼科 眼科
- 耳鼻喉科 耳鼻喉科 耳鼻喉科
背景情况:
- 苏萨克综合征 (SuS) 是一种罕见的免疫媒介性内皮病,影响大脑,视网膜和内耳微血管.
- 它典型地呈现出脑病变,分支视网膜动脉封闭和感觉神经听力损失的三位一体.
研究的目的:
- 描述被诊断患有苏萨克综合征的患者的听觉静脉干扰.
- 确定与SUS相关的特定听力学和前庭检测结果.
主要方法:
- 对21名SUS患者的电子病历进行了回顾性审查.
- 收集的数据包括人口统计,临床表现,疾病过程和音频口腔检测结果.
主要成果:
- 所有21名患者都报告了听觉静脉病情,最常见的是,不稳定,听力损失,耳和听觉充实.
- 15名患者表现出感应神经听力损失 (主要是低频到中频),8/18人表现出前庭异常 (例如,前庭唤起肌原潜力).
- 进行了广泛的免疫抑制疗法,听力损失通常保持温和.
结论:
- 听觉静脉功能障碍在苏萨克综合征中非常普遍.
- 典型的发现包括"反向倾斜"听力损失和耳膜功能障碍.
- 早期识别和积极的免疫抑制对于管理SUS和潜在地保护内耳功能至关重要.
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