Jove
Visualize
联系我们
JoVE
x logofacebook logolinkedin logoyoutube logo
关于 JoVE
概览领导团队博客JoVE 帮助中心
作者
出版流程编辑委员会范围与政策同行评审常见问题投稿
图书馆员
用户评价订阅访问资源图书馆顾问委员会常见问题
研究
JoVE JournalMethods CollectionsJoVE Encyclopedia of Experiments存档
教育
JoVE CoreJoVE BusinessJoVE Science EducationJoVE Lab Manual教师资源中心教师网站
使用条款与条件
隐私政策
政策

相关概念视频

Myasthenia Gravis: Diagnostic Tests01:15

Myasthenia Gravis: Diagnostic Tests

686
Myasthenia gravis is an autoimmune condition affecting neuromuscular transmission, causing generalized weakness in skeletal muscles. Initial diagnoses rely on patients' signs, symptoms, and medical history. The challenge lies in distinguishing myasthenia from other muscular dystrophies. An important diagnostic feature is the significant improvement of symptoms after administering anticholinesterase inhibitors.
The edrophonium test is a diagnostic tool for myasthenia gravis. It involves...
686

您也可能阅读

相关文章

通过共同作者、期刊和引用图与本文相关的文章。

排序
Same author

Frontiers in movement disorder therapeutics: A new era in neurology.

Clinical parkinsonism & related disorders·2025
Same author

Tardive dyskinesia versus tardive syndrome. What is in a name?

Parkinsonism & related disorders·2025
Same author

Patient selection and injection techniques for botulinum neurotoxin in oromandibular dystonia.

Clinical parkinsonism & related disorders·2022
Same author

Medications used to treat tremors.

Journal of the neurological sciences·2022
Same author

Parkinsonism in viral, paraneoplastic, and autoimmune diseases.

Journal of the neurological sciences·2021
Same author

Editorial "Parkinsonism across the spectrum of movement disorders and beyond".

Journal of the neurological sciences·2021
Same journal

Hyperkinetic manifestations in sporadic parkinsonism: An exploratory case series with APOE and NOS3 variants.

Clinical parkinsonism & related disorders·2026
Same journal

Clinical and autonomic correlates of chronic Sialorrhea in Parkinson's disease: a questionnaire-based study with cluster analysis of autonomic and dysphagia burden.

Clinical parkinsonism & related disorders·2026
Same journal

Cerebral hemodynamic changes and their effects on cognitive function in patients with Parkinson's disease complicated with orthostatic hypotension.

Clinical parkinsonism & related disorders·2026
Same journal

Mark Hallett: scientist and humanitarian in modern movement disorder neurology.

Clinical parkinsonism & related disorders·2026
Same journal

Factors influencing receipt of specialty neurologic care for patients with Huntington's disease in Colorado.

Clinical parkinsonism & related disorders·2026
Same journal

Mark Hallett and the renaissance of functional neurological disorder.

Clinical parkinsonism & related disorders·2026
查看所有相关文章

相关实验视频

Updated: Jun 11, 2025

Abbiategrasso Brain Bank Protocol for Collecting, Processing and Characterizing Aging Brains
12:28

Abbiategrasso Brain Bank Protocol for Collecting, Processing and Characterizing Aging Brains

Published on: June 3, 2020

17.3K

多重系统缩:诊断挑战和一个建议的诊断算法.

Deepmala Nandanwar1, Daniel D Truong1

  • 1The Parkinson and Movement Disorder Institute, 9940 Talbert Avenue, Fountain Valley, CA 92708, USA.

Clinical parkinsonism & related disorders
|October 9, 2024
PubMed
概括
此摘要是机器生成的。

多重系统缩 (MSA) 是一种同核病变,表现为自主功能障碍,帕金森症或动脉缩. 这项研究提出了一种诊断算法,用于指导MSA诊断的MRI和自主测试等测试的使用.

更多相关视频

Utility of Dissociated Intrinsic Hand Muscle Atrophy in the Diagnosis of Amyotrophic Lateral Sclerosis
08:16

Utility of Dissociated Intrinsic Hand Muscle Atrophy in the Diagnosis of Amyotrophic Lateral Sclerosis

Published on: March 4, 2014

31.7K
Comprehensive Autopsy Program for Individuals with Multiple Sclerosis
09:41

Comprehensive Autopsy Program for Individuals with Multiple Sclerosis

Published on: July 19, 2019

11.4K

相关实验视频

Last Updated: Jun 11, 2025

Abbiategrasso Brain Bank Protocol for Collecting, Processing and Characterizing Aging Brains
12:28

Abbiategrasso Brain Bank Protocol for Collecting, Processing and Characterizing Aging Brains

Published on: June 3, 2020

17.3K
Utility of Dissociated Intrinsic Hand Muscle Atrophy in the Diagnosis of Amyotrophic Lateral Sclerosis
08:16

Utility of Dissociated Intrinsic Hand Muscle Atrophy in the Diagnosis of Amyotrophic Lateral Sclerosis

Published on: March 4, 2014

31.7K
Comprehensive Autopsy Program for Individuals with Multiple Sclerosis
09:41

Comprehensive Autopsy Program for Individuals with Multiple Sclerosis

Published on: July 19, 2019

11.4K

科学领域:

  • 神经学 神经学
  • 病理学 病理学 病理学
  • 诊断成像 诊断成像 诊断成像

背景情况:

  • 多重系统缩 (MSA) 是一种罕见的,致命的神经退行性疾病,其特点是自主功能障碍,帕金森症和小脑缩.
  • MSA与帕金森病 (PD) 和莱维体痴呆症 (DLB) 具有共同的病理特征,它们被统称为同核蛋白病变.
  • 阿尔法-同核素质细胞质内含是MSA的病理标志,可以在皮肤活检中检测到.

研究的目的:

  • 提出一个多系统缩 (MSA) 的诊断算法.
  • 为了澄清MSA评估中诊断测试的适当使用.
  • 帮助临床医生将MSA与其他神经疾病区分开来.

主要方法:

  • 审查目前的MSA诊断工具,包括大脑MRI,心脏MIBG扫描,自主功能测试和尿动力学研究.
  • 开发一种诊断算法,以指导这些研究的顺序或并行使用.
  • 拟议的算法与现有的运动障碍学会 (MDS) 对MSA的诊断标准进行比较.

主要成果:

  • 脑部MRI发现,如"热十字面包"标志,胺缩和骨内异常,可以支持MSA诊断.
  • 特定的测试,如心脏MIBG扫描,自主测试和尿动力学研究对于区分MSA与其他疾病至关重要.
  • 拟议的算法提供了一个结构化的方法,用于在疑似MSA病例中进行诊断测试.

结论:

  • 对于MSA,有可用的诊断工具,但它们的最佳应用需要明确的指导.
  • 建议的算法旨在增强MSA的诊断过程,补充现有标准.
  • 对诊断算法的进一步改进和验证可能会改善早期和准确的MSA诊断.