严重获得的第七因子缺乏症复杂化了无塑性贫血,成功地用皮质类固醇治疗
Romain Batton1, Chamouni Pierre2, Marion Carrette3
1CHU Rouen, Department of Internal Medicine.
概括
获得的第七因子缺乏症 (aFVII) 是罕见的,经常出现出血. 这一案例突出了老年患者患有无塑性贫血的aFVII,强调了需要更好的治疗指南的需要.
科学领域:
- 血液学 血液学 血液学
- 内部医学 内部医学
- 罕见疾病 罕见疾病
背景情况:
- 因子VII缺乏症是一种罕见的静血性疾病,由于病例报告有限,治疗指南不清楚.
- 获得的第七因子缺乏症 (aFVII) 异常罕见,特别是在老年人中.
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