肺动脉孤立单边缺失 (IUAPA) 与渐进的间歇性阴影呈现:一个病例报告
Tomohito Takeshige1,2, Ryo Koyama1, Makiko Kohmaru1
1Department of Respiratory Medicine Juntendo University Nerima Hospital Tokyo Japan.
Respirology case reports
|October 17, 2024
概括
肺动脉孤立单边缺失 (IUAPA) 是一种罕见的先天性疾病,通常在生命晚期被诊断出来. 这一案例凸显了识别非特异性症状的成年人血管异常的重要性.
科学领域:
- 心脏病学 心脏病学
- 放射学 放射学是一门学科.
- 肺部病理学 肺部病理学
背景情况:
- 肺动脉单侧缺失 (UAPA) 是一种罕见的先天性异常.
- 孤立的UAPA (IUAPA) 发生在没有先天性心脏病的情况下,并且通常在成年时被诊断出来.
- 像胸痛和间歇性肺阴影等非特定症状可以掩盖IUAPA.
研究的目的:
- 报告在成年后期诊断的IUAPA病例.
- 强调在IUAPA中血管成像的诊断挑战和重要性.
- 为了突出慢性,非特异性症状的患者的延迟诊断.
主要方法:
- 一个61岁的女性患者的病例报告.
- 临床表现包括右胸部疼痛和9年间间歇性阴影恶化.
- 通过对比增强计算机断层扫描 (CECT) 证实了诊断,揭示了肺动脉向右肺流动的缺失.
主要成果:
- 这位患者在经历了大约40年的症状后被诊断出患有IUAPA.
- CECT显示,肺动脉向右肺的血液流动明显缺失.
- 这些发现强调了IUAPA的显著诊断延迟的可能性.
结论:
- 应考虑在患有持续,非特异性呼吸道或胸部症状和放射性异常的成年人中使用IUAPA.
- 像CECT这样的先进成像技术对于识别肺血管异常至关重要.
- 早期识别IUAPA可以防止长期的诊断旅程,并指导适当的管理.
相关概念视频
Pulmonary Embolism I: Introduction
2
Pulmonary embolism (PE) occurs when a thrombus, fat or air embolus, amniotic fluid, or tumor tissue blocks one or more pulmonary arteries. These blockages originate in the venous system or the right side of the heart.EtiologyPE primarily arises from deep vein thrombosis (DVT) and other hypercoagulable states, such as inherited thrombophilias. Additional etiological factors include venous stasis, commonly seen in obesity, and endothelial injury from surgery and trauma. Less common causes include...
2
Mitral Stenosis I: Introduction
2
Mitral Valve Stenosis (MVS) is a heart condition where the mitral valve narrows, impeding blood circulation from the left atrium to the left ventricle. The etiology and pathophysiology of this condition are multifaceted, leading to a cascade of cardiovascular complications.Causes of Mitral Valve StenosisRheumatic Heart Disease: It is the main cause of mitral valve stenosis, particularly in developing nations. This condition arises from rheumatic fever, an inflammatory illness resulting from...
2
Imaging Studies for Cardiovascular System III: X-Ray
149
The most common cardiovascular diagnostic test is an X-ray. It produces images of the heart, blood vessels, and adjacent structures.
Definition and Purpose
An X-ray, or radiograph, is a non-invasive method that uses ionizing radiation to take images of internal structures. It is mainly used in cardiac imaging to examine the heart, lungs, and major blood vessels, aiming to identify abnormalities in the heart's size, shape, and position, such as heart failure, congenital defects, and vascular...
Definition and Purpose
An X-ray, or radiograph, is a non-invasive method that uses ionizing radiation to take images of internal structures. It is mainly used in cardiac imaging to examine the heart, lungs, and major blood vessels, aiming to identify abnormalities in the heart's size, shape, and position, such as heart failure, congenital defects, and vascular...
149
Pulmonary Tuberculosis II
212
Tuberculosis, or TB, is a bacterial infectious disease caused by Mycobacterium tuberculosis. While its primary impact is on the lungs, leading to pulmonary tuberculosis, it can also affect various other organs, a condition referred to as extrapulmonary tuberculosis.
Here is a detailed explanation of its pathophysiology:
Transmission: The process begins when a person inhales droplet nuclei containing M. tuberculosis. These are typically released into the air when an individual with pulmonary or...
Here is a detailed explanation of its pathophysiology:
Transmission: The process begins when a person inhales droplet nuclei containing M. tuberculosis. These are typically released into the air when an individual with pulmonary or...
212
Pericarditis II: Clinical features and Diagnostic Tests
3
Pericarditis is distinguished by inflammation of the pericardium, the fibrous sac that encases the heart. It can be acute, lasting less than six weeks, or chronic, persisting for over three months. Understanding its clinical manifestations and diagnostic findings is crucial for timely and effective management.Clinical ManifestationsWhile pericarditis can be asymptomatic, it usually presents with characteristic symptoms such as:Chest Pain: The most characteristic symptom of pericarditis is chest...
3
Pneumothorax-II
123
Pneumothorax is a medical condition defined by the buildup of air in the pleural space between the lungs and the chest wall. This accumulation of air can lead to partial or complete lung collapse, resulting in a range of clinical manifestations. Understanding the clinical presentation and effective management strategies is crucial for healthcare professionals in providing timely and appropriate care to individuals with pneumothorax.
Clinical Manifestations:
Clinical Manifestations:
123


