延迟诊断Herlyn-Werner-Wunderlich综合征与双边角的扩散性腺化
Roshna Adhikari1, Mukesh Paudel1, Saroj Sharma1
1National Academy of Medical Sciences, Bir Hospital, Kathmandu, Nepal.
Radiology case reports
|October 21, 2024
概括
赫林-沃纳-万德利希综合征是一种罕见的先天性疾病,涉及子宫大和阻塞的半阴道. 这一案例突显了一个43岁的女性晚期诊断患有相关腺菌症,强调了需要准确诊断和治疗的必要性.
科学领域:
- 生殖医学 生殖医学
- 妇科外科手术 妇科外科
- 医疗成像医学成像
背景情况:
- 赫林-沃纳-万德利希综合征 (HWW) 是一种罕见的先天性异常,其特征是子宫大,单侧阻塞的半阴道和双侧衰.
- 通常在青春期出现骨盆疼痛和由于血栓塞或血液计的异常潮,HWW综合征也可以在成年时表现为不孕症.
- 潜在的并发症包括pyohematocolpos,pyosalpinx,盆腔炎,子宫内膜炎,以及堕胎和不孕症的风险增加.
研究的目的:
- 介绍一个43岁女性晚期诊断的Herlyn-Werner-Wunderlich综合征病例.
- 为了突出扩散双边腺核瘤与HWW综合征的不常见关联.
- 讨论这个复杂的妇科异常的诊断和治疗方法.
主要方法:
- 通过超声波进行初步检查,以确定子宫异常,代和血栓塞.
- 使用磁共振成像 (MRI) 确认诊断和详细解剖评估.
- 手术管理涉及阴道隔膜切除阻塞的半阴道和腺菌症的荷尔蒙治疗.
主要成果:
- 一名43岁的女性出现了循环性经期不良,子宫 didelphys,左侧阴道隔膜与血栓塞,和左侧衰老.
- 由于先前的错误诊断,患者的诊断迟到了.
- 分散双边腺核瘤症被确定为一种不常见的共存疾病.
结论:
- 阴道隔膜切除是症状性HWW综合征的主要治疗方法.
- 晚期诊断HWW综合征可能会发生,特别是当它与诸如腺髓炎等疾病相关时.
- 准确的成像和及时的干预对于管理HWW综合征及其并发症至关重要.
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