ADAMTS13,线

Emmanuel J Favaloro1,2,3, Leonardo Pasalic1,4, Giuseppe Lippi5

  • 1Department of Haematology, Sydney Centres for Thrombosis and Haemostasis, Institute of Clinical Pathology and Medical Research (ICPMR), Westmead Hospital, Westmead, NSW, Australia.

概括

缺乏ADAMTS13酶可以导致血栓性血栓细胞衰竭紫外线 (TTP) 和其他血栓性微血管病变 (TMA). 对ADAMTS13及其抗体的实验室检测对于诊断和管理这些疾病至关重要.