在喉-气管支气管粉样蛋白中保持警的等待:一个病例报告
Dylan Beinart1,2, Siaw Ming Chai3, Olivia Walsh1,2
1Department of Respiratory Medicine Sir Charles Gairdner Hospital Perth Western Australia Australia.
Respirology case reports
|November 5, 2024
概括
这一案例研究跟踪了一名66岁的男性,患有喉-气管支气管 Amyloidosis. 他的呼吸功能在13年内保持稳定,不需要任何干预.
科学领域:
- 呼吸系统医学 呼吸系统医学
- 肺部病理学 肺部病理学
- 医疗病例报告 病例报告
背景情况:
- 喉 - 气管 - 支气管 Amyloidosis 是一种罕见的疾病.
- 最初的错误诊断可能会推迟适当的治疗.
- 对于罕见的呼吸道疾病而言,长期跟踪至关重要.
研究的目的:
- 报告一个患有喉-气管支气管 Amyloidosis 的患者13年的随访情况.
- 突出特定患者疾病的自然过程.
- 强调成像在诊断呼吸道疾病的重要性.
主要方法:
- 一个纵向的案例研究.
- 审查患者的病史和诊断成像.
- 肺功能测试 (FEV1和FVC) 超过13年.
主要成果:
- 一名66岁的男性患有喉-气管支气管 Amyloidosis 在13年内表现出稳定的FEV1和FVC.
- 截面胸部成像揭示了远端气管和近端主要支气管的扩散加厚.
- 在随访期间,不需要进行医疗或手术干预.
结论:
- 在一些患者中,喉-气管支气管粉样性粉症可能具有稳定的临床过程.
- 肺功能可以保持稳定,尽管有显著的气道加厚.
- 保守的管理可能适用于喉-气管支气管 Amyloidosis 的选择病例.
相关概念视频
Endoscopic Studies II: Thoracocentesis
206
Thoracentesis(Thoracocentesis), commonly known as pleural tap, is a medical procedure where a 22 gauge needle is inserted into the pleural space, the area between the lung and chest wall. This procedure is commonly performed to diagnose or treat various respiratory disorders.
Description
Excess pleural fluid or air may accumulate in some respiratory disorders in the thoracic cavity. To treat pleural effusion, a physician conducts thoracentesis by carefully piercing the chest wall and entering...
Description
Excess pleural fluid or air may accumulate in some respiratory disorders in the thoracic cavity. To treat pleural effusion, a physician conducts thoracentesis by carefully piercing the chest wall and entering...
206
Tracheostomy Care II: Procedure
122
Tracheostomy care is an essential nursing skill that involves cleaning and maintaining a tracheostomy tube to prevent infection and other complications. Here's a step-by-step guide explaining each procedure with its rationale. Note that disposable gloves are to be worn at all times and changed as often as needed to maintain a sterile work environment, and to protect both patient and healthcare worker.
Step 1: Perform hand hygiene, and put on personal protective equipment: gown, gloves, mask...
Step 1: Perform hand hygiene, and put on personal protective equipment: gown, gloves, mask...
122
Endoscopic Studies I: Bronchoscopy and Thoracoscopy
173
Endoscopy is a non-surgical medical technique used to examine a person's internal organs and vessels. This lesson will focus on two types of endoscopic studies: bronchoscopy and thoracoscopy.
Bronchoscopy
Description
Bronchoscopy is a procedure that involves direct visualization of the larynx, trachea, and bronchi for diagnostic and therapeutic purposes. A flexible fiber optic or rigid bronchoscope is used to carry out the procedure. The fiber-optic bronchoscope is more frequently used due...
Bronchoscopy
Description
Bronchoscopy is a procedure that involves direct visualization of the larynx, trachea, and bronchi for diagnostic and therapeutic purposes. A flexible fiber optic or rigid bronchoscope is used to carry out the procedure. The fiber-optic bronchoscope is more frequently used due...
173
Respiratory System Abnormal Finding II: Palpation and Auscultation
275
In assessing respiratory abnormalities, palpation and auscultation are critical tools for detecting and interpreting various pathophysiological changes. These techniques provide insight into underlying disorders by evaluating tactile sensations and sounds produced by the respiratory system.
Palpation Findings
During a respiratory assessment, palpation can reveal several vital abnormalities:
Palpation Findings
During a respiratory assessment, palpation can reveal several vital abnormalities:
275


