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携带FLNA功能丧失变体的患者的肺高血压

Laura Stourm1,2,3, Julien Grynblat4,5,6,3, Laurent Savale5,6,7

  • 1Department of Respiratory Diseases, Le Mans General Hospital, Le Mans, France.

The European respiratory journal
|November 7, 2024
PubMed
概括

纤维素A (FLNA) 功能丧失变体中的肺高血压 (PH) 是一个严重的并发症. 对于PH和相关症状的患者来说,FLNA早期遗传查至关重要.

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