意想不到的正常ROTEM导致蛋白C缺乏与IVC血栓形成
Rachel Seunah Kim1, Uzung Yoon2
1Anesthesiology, Thomas Jefferson University Hospitals, Philadelphia, Pennsylvania, USA rachelseunah@gmail.com.
BMJ case reports
|November 17, 2024
概括
蛋白C缺乏症是一种遗传性疾病,对旋转性血栓形成显微镜 (ROTEM) 分析有复杂的影响. 尽管有这种情况,但一个病人表现出正常的凝血结果,突出显示了身体保持平衡的能力.
科学领域:
- 血液学 血液学 血液学
- 血管外科 血管外科
- 临床凝血 临床凝血
背景情况:
- 蛋白C缺乏症是一种与血栓形成风险增加相关的遗传性疾病.
- 蛋白C缺乏对旋转性血栓等离体计 (ROTEM) 参数的影响仍然不完全理解.
- 患有血栓性疾病的患者通常需要复杂的手术干预和监测.
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