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Updated: Jun 6, 2025

In Vitro Enzyme Measurement to Test Pharmacological Chaperone Responsiveness in Fabry and Pompe Disease
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In Vitro Enzyme Measurement to Test Pharmacological Chaperone Responsiveness in Fabry and Pompe Disease

Published on: December 20, 2017

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补充系统和粘附分子在法布里病中的争斗:对病原和疾病机制的洞察

Albert Frank Magnusen1, Manoj Kumar Pandey1,2

  • 1Division of Human Genetics, Cincinnati Children's Hospital Medical Center, Cincinnati, OH 45229, USA.

International journal of molecular sciences
|November 27, 2024
PubMed
概括

费布里病涉及全球基胺的积累,激活补充系统. 向补充成分C3a和C5a可能会减少炎症并改善Fabry患者的结果.

关键词:
细胞粘附分子的细胞粘附分子补充介导的伤害是补充介导的伤害.内皮质功能障碍 在内皮质功能障碍免疫细胞的透.这是一种炎症级联.

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