人类CFTR缺陷的iPSC巨细胞在感染Pseudomonas aeruginosa时显示功能和转录基因反应受损

Claudio Rodriguez Gonzalez1, Débora Basílio-Queirós1, Anna-Lena Neehus2,3,4,5,6

  • 1Department of Pediatric Pneumology, Allergology and Neonatology, Hannover Medical School, Hannover, Germany.

Frontiers in immunology
|November 28, 2024
PubMed
概括

囊性纤维化巨细胞表现出细菌清除受损和炎症增加. 这项研究引入了一种新的人类诱导的多能干细胞衍生巨细胞模型,用于调查CFTR.