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Updated: Jun 6, 2025

Imaging Features of Systemic Sclerosis-Associated Interstitial Lung Disease
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系统性硬化症相关的和异常性肺动脉高血压之间的病理差异.

Samuel H Friedman1, Russell A Harley2, Jacob Williams3

  • 1Division of Pulmonary, Critical Care, Allergy and Sleep Medicine, Department of Medicine, Medical University of South Carolina, Charleston, SC, USA.

Journal of scleroderma and related disorders
|December 2, 2024
PubMed
概括

与系统性硬化症相关的肺动脉高血压相比,肺部表现出明显的间歇性纤维化和免疫细胞透,而非异常性肺动脉高血压. 这些差异可能解释了肺动脉高血压患者治疗反应的不同.

关键词:
IPAH IPAH 是一个这些PAH是PAH.这就是SSc-PAH.免疫组织化学 免疫组织化学硬化皮质硬化皮质 (scleroderma) 是一种疾病.

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