在阿尔法-2-抗等离子素缺乏患者中增强的血栓和等离子素生成概况:来自荷兰罕见出血障碍研究的数据

Bauke Haisma1,2, Sanna R Rijpma2,3, Marjon H Cnossen4

  • 1Department of Hematology, Radboud University Medical Center, Nijmegen, the Netherlands.

概括

阿尔法2-抗等离子素 (A2AP) 缺乏导致纤维素分解和出血的增加. 这项研究发现,A2AP缺乏症患者表现出高血和血栓生成,与出血严重程度相关.

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