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Updated: Jun 5, 2025

Assessment of Open Probability of the Mitochondrial Permeability Transition Pore in the Setting of Coenzyme Q Excess
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Published on: June 1, 2022

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通过m-AAA蛋白酶和禁止因复合体对线粒体通道的蛋白质分解调节

Alaumy Joshi1, Rachel A Stanfield1, Andrew T Spletter1

  • 1Department of Biochemistry and Biophysics, Texas A&M University, 301 Old Main Drive, MS 3474, College Station, TX 77843, USA.

Genetics
|December 10, 2024
PubMed
概括

研究人员确定了一种关键的蛋白质复合物,m-AAA蛋白酶/禁素,它降解了线粒体通道MRS2. 准这种复合体可以恢复心脂素贫乏细胞中的MRS2水平,从而提供对巴斯综合征的见解.

关键词:
m-AAAA蛋白酶的使用情况.线粒体中的线粒体.这位女士是 Mrs2 Mrs2卡尔迪奥利平因 (cardiolipin) 是一种心脏质蛋白质.禁止使用禁止使用.

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