图像检测结果和管理策略对于患有倾向障碍的儿童的肝脏质量:由儿科LI-RADS小组的审查
Amy B Kolbe1, Michael R Acord1, Geetika Khanna1
1From the Department of Radiology, Mayo Clinic, 200 1st Ave SE, Rochester, MN 55905 (A.B.K.); Department of Radiology, Children's Hospital of Philadelphia, University of Pennsylvania Perelman School of Medicine, Philadelphia, Pa (M.R.A.); Department of Radiology and Imaging Sciences, Emory University and Children's Healthcare of Atlanta, Atlanta, Ga (G.K., A.A.); Department of Radiology, Cincinnati Children's Hospital, Department of Radiology, University of Cincinnati College of Medicine, Cincinnati, Ohio (C.E.M., A.J.T.); Department of Radiology, Keck School of Medicine and Children's Hospital Los Angeles, Los Angeles, Calif (H.N.N.); Department of Radiology, Nationwide Children's Hospital, Columbus, Ohio (M.A.R.); Department of Medical Imaging, Ann and Robert H. Lurie Children's Hospital of Chicago, Chicago, Ill (E.R.); Department of Radiology, UT Southwestern Medical Center, Dallas, Tex (G.R.S.); Department of Radiology, UPMC Children's Hospital of Pittsburgh, Pittsburgh, Pa (J.H.S.); Department of Radiology, Stanford University School of Medicine, Stanford, Calif (A.B.S.); and Department of Radiology, Children's Hospital Colorado, Aurora, Colo (E.R.T.).
儿童肝脏质量,从良性到肝细胞癌 (HCC),与全身性疾病和综合征有关. 放射科医生使用成像来指导诊断和查这些肝病变.
科学领域:
- 儿科放射学 儿科放射学
- 医学遗传学 医学遗传学
- 肝病学 肝病学是一种肝病学.
背景情况:
- 患有全身性疾病或倾向性综合征的儿童可以发展良性或恶性肝脏质量.
- 了解潜在的疾病及其对肝脏的影响对于准确的诊断和管理至关重要.
- 已经确立的成像查指南存在于特定的遗传疾病,如贝克维思·维德曼谱.
研究的目的:
- 总结患有易感综合征和全身性疾病的儿童肝病变的范围.
- 描述这些病变在各种模式中的成像外观.
- 审查已公布的儿童肝脏质量查指南.
主要方法:
- 关于与全身性疾病和综合征相关的儿科肝脏质量的文献综述.
- 分析各种肝病变的成像特征.
- 编制现有的查建议和指导方针.
主要成果:
- 儿童的肝脏质量从焦点脂肪到肝细胞癌 (HCC) 不同.
- 成像在指导治疗方式选择,频率和活检建议方面发挥着关键作用.
- 对于某些综合征,已经制定了查指南,而对于其他综合征则缺乏共识,通常基于肝硬化和HCC风险.
结论:
- 放射科医生对潜在疾病的了解有助于管理儿科肝脏质量.
- 图像监测是必不可少的,特别是在患有慢性肝病和肝细胞癌的儿童中.
- 对于没有确立指南的综合征,需要进一步就查达成共识.


