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Updated: Jun 5, 2025

Targeting Cysteine Thiols for in Vitro Site-specific Glycosylation of Recombinant Proteins
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在微小的甘油三转移蛋白中,一种新的突变,Ile344Asn,取消了与蛋白质二硫化物异构酶的结合

Swati Valmiki1, Cindy Bredefeld2, M Mahmood Hussain1

  • 1Department of Foundations of Medicine, NYU Grossman Long Island School of Medicine, Mineola, NY, USA.

Journal of lipid research
|December 13, 2024
PubMed
概括

微体甘油转移蛋白 (MTP) 突变导致阿贝塔利波蛋白血症. 一种新的MTP突变,Ile344Asn,破坏了MTP:PDI相互作用,损害了脂质转移和阿波利波蛋白B分泌.

关键词:
一个betalipoproteinemia是什么意思在 apoBB 的时候.低贝塔利波蛋白质血症 (hypobetalipoproteinemia) 是一种疾病.脂蛋白质是一种脂蛋白质.变种变种的变种

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