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Updated: Jun 10, 2026

An In Vitro Model for the Study of Cellular Pathophysiology in Globoid Cell Leukodystrophy
07:45

An In Vitro Model for the Study of Cellular Pathophysiology in Globoid Cell Leukodystrophy

Published on: October 21, 2014

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吉尔丁缺乏症会导致发育性和性脑病变,带有海马硬化和内神经病变

Machiko Iida1, Motoki Tanaka1, Tsuyoshi Takagi1

  • 1Department of Disease Model, Institute for Developmental Research, Aichi Developmental Disability Center, Kasugai, Aichi, Japan.

Epilepsia
|December 15, 2024
PubMed
概括

一种新的食方案允许Girdin/CCDC88A淘汰小鼠生存,揭示了发育性脑病变 (DEE) 的机制. 这种模型使得研究与海马硬化和内神经病变的研究成为可能.

关键词:
Nkx2‐1‐1 的情况.动物模型动物模型半径叶发作 半径叶发作迁移缺陷是一个迁移缺陷.帕尔瓦胺-内部神经元

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Transplantation of Human Stem Cell-Derived GABAergic Neurons into the Early Postnatal Mouse Hippocampus to Mitigate Neurodevelopmental Disorders05:00

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