成年人的先天性单管大动脉:小型综述和病例系列
Ashraf Mohammed Anwar1,2, Hattan H Alshawkani1, Ibrahim Albakri1
1Department of Cardiology, King Fahad Armed Forces Hospital, Jeddah, Saudi Arabia.
Annals of pediatric cardiology
|December 19, 2024
概括
单主动脉 (UAV) 是一种罕见的先天性心脏缺陷. 本综述涵盖无人机亚型,诊断和管理,介绍了四个成年病例,干预和结果各不相同.
科学领域:
- 心脏病学 心脏病学
- 遗传性心脏病是一种先天性心脏病.
- 心脏外科手术 心脏外科手术
背景情况:
- 单主动脉 (UAV) 是一种极为罕见的主动脉 (AV) 的先天性形.
- 无人机呈现出不同的亚型:commissural和unicommissural,不同的解剖特征,成像特征和临床表现.
- 严重的大动脉损伤需要及时进行手术或透导管干预.
研究的目的:
- 为了提供一个全面的对单主动脉的综述,包括解剖特征,临床表现,诊断方式和管理策略.
- 介绍一系列四名被诊断患有UAV的成年患者,说明不同的临床疗程和治疗方法.
主要方法:
- 文献综述总结了关于无人机的当前知识.
- 病例系列详细介绍了四名成年无人机患者,包括他们的病史,诊断结果和治疗结果.
- 在所有提出的病例中,用于最终诊断和功能评估的跨食道心声学 (TEE).
主要成果:
- 该审查涵盖了无人机的解剖学,临床谱,诊断工具和管理选项.
- 分析了四个成年无人机的案例:三个单独的和一个非单独的.
- 患者的治疗结果各不相同,包括儿童气球膜整形术,随后进行门置换,罗斯手术,以及对无症状的中度狭窄或轻度至中度吐的无症状个体进行保守的治疗.
结论:
- 单主动脉需要对其亚型和临床影响有充分的了解.
- 像TEE这样的诊断模式对于准确的无人机评估至关重要.
- 无人机的管理策略应根据门形态,病变严重程度和患者表现进行个性化,从警等待到复杂的外科干预.
更多相关视频
12:17Full-root Aortic Valve Replacement by Stentless Aortic Xenografts in Patients with Small Aortic Roots
Published on: May 21, 2017
11.3K
13:10Direct Re-implantation of Left Coronary Artery into the Aorta in Adults with Anomalous Origin of Left Coronary Artery from the Pulmonary Artery ALCAPA
Published on: April 24, 2017
18.5K
相关概念视频
01:22Mitral Stenosis I: Introduction
1
Mitral Valve Stenosis (MVS) is a heart condition where the mitral valve narrows, impeding blood circulation from the left atrium to the left ventricle. The etiology and pathophysiology of this condition are multifaceted, leading to a cascade of cardiovascular complications.Causes of Mitral Valve StenosisRheumatic Heart Disease: It is the main cause of mitral valve stenosis, particularly in developing nations. This condition arises from rheumatic fever, an inflammatory illness resulting from...
1
01:23Mitral Regurgitation II: Clinical features and Diagnostic Tests
1
Mitral regurgitation (MR) is a valvular heart disorder in which the mitral valve fails to close tightly, allowing blood to leak backward into the heart. Understanding the clinical manifestations, assessment, diagnostic findings, and medical management of MR is crucial to effectively managing affected patients.Clinical Manifestations of Mitral RegurgitationMitral regurgitation can be acute or chronic, each presenting differently and requiring different approaches:1. Acute Mitral...
1
01:20Mitral Regurgitation I: Introduction
1
Mitral regurgitation is characterized by the backward circulation of blood from the left ventricle to the left atrium during systole, a phase of the cardiac cycle when the heart contracts and pumps blood out of the chambers. This abnormal flow occurs primarily due to the dysfunction of the mitral valve or its supporting structures, which include the mitral leaflets, chordae tendineae, annulus, and papillary muscles.Etiology and Mechanisms:Primary Mitral Regurgitation: This type arises from...
1
01:22Mitral Valve Prolapse II: Assessment and Management
1
IntroductionA range of clinical features characterizes Mitral Valve Prolapse (MVP), but it is important to note that many individuals with MVP are asymptomatic and may remain so throughout their lives. For those who do exhibit symptoms, the following are the key clinical features:Palpitations: This is a common symptom where individuals feel an irregular or rapid heartbeat. Palpitations in MVP are often due to arrhythmias such as premature ventricular contractions or supraventricular...
1
01:16Heart Valves
4.3K
The human heart is a complex organ with an intricate system of valves that regulate blood flow. There are two main types of valves: atrioventricular (AV) valves and semilunar valves.
The AV valves prevent the backflow of blood from the ventricles to the atria during ventricular contraction. These valves function with the assistance of the chordae tendineae and papillary muscles. When the ventricles are relaxed, the chordae tendineae are slack, allowing blood to flow from the atria into the...
The AV valves prevent the backflow of blood from the ventricles to the atria during ventricular contraction. These valves function with the assistance of the chordae tendineae and papillary muscles. When the ventricles are relaxed, the chordae tendineae are slack, allowing blood to flow from the atria into the...
4.3K
01:27Mitral Valve Prolapse I: Introduction
1
IntroductionThe mitral valve, one of the heart's four valves, regulates blood flow. These valves have flaps that open and close to direct blood properly through the heart and body. During each heartbeat, the flaps open for blood to pass through and seal shut to prevent backflow. Specifically, the mitral valve opens to allow blood flow from the heart's upper left chamber to the lower left chamber. It then closes securely as the lower left chamber contracts to pump blood to the body, preventing...
1