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Updated: Jun 3, 2025

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在中国,囊性纤维化患者的进展和死亡率

Wangji Zhou1, Yaqi Wang1, Yanli Yang1

  • 1Department of Pulmonary and Critical Care Medicine, State Key Laboratory of Complex Severe and Rare Diseases, State Key Laboratory of Common Mechanism Research for Maior Diseases, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, China.

Orphanet journal of rare diseases
|January 8, 2025
PubMed
概括

这项研究详细介绍了中国的囊性纤维化 (CF) 进展和死亡率. 基线肺功能和恶化影响CF患者的结果,预后得分有助于生存预测.

关键词:
华人中文 华人中文是什么意思囊性纤维化症是什么肺功能 肺功能 肺功能死亡率 死亡率 死亡率预测 预后 预测 预测

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