肺膜蛋白质症:与巨细胞功能障碍相关的罕见疾病的临床和形态概述

Brigita Javorská1, Róbert Slivka1, Barbora Durcová1,2

  • 1Second Department of Pneumology and Phthisiology, National Institute for Tuberculosis, Lung Diseases and Thoracic Surgery in Vyšné Hágy, Vysoké Tatry, Slovakia.

PubMed
概括

肺膜蛋白质症 (PAP) 是一种罕见的肺部疾病,由表面活性剂的积累引起. 研究强调了花细胞-巨细胞殖民地刺激因子 (GM-CSF) 在PAP病原和潜在疗法的作用.

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