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在 lysosomal 存储疾病中神经退行症的统一生物学

Anna M Ludlaim1, Simon N Waddington2,3, Tristan R McKay1

  • 1Department of Life Sciences, Manchester Metropolitan University, Manchester, UK.

Journal of inherited metabolic disease
|January 17, 2025
PubMed
概括

具有神经退行性的溶解体储存疾病 (LSD) 尽管有不同的遗传原因,但具有共同的途径. 了解这些共享机制是开发治疗这些衰弱性脑疾病的关键.

关键词:
费布里病是什么意思 费布里病是什么意思戈舍氏病是戈舍氏病的一种疾病.Krabbe 的疾病 病.尼曼 - 皮克的选择.桑德霍夫 (Sandhoff) 公司泰·萨克斯 (Tay-Sachs) 是一个lysosomal 储存疾病 lysosomal 储存疾病甲基染色性白血病变异症是什么粘多糖糖症 粘多糖糖症神经神经元的seroid lipofuscinosis 发生在神经元中.

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