二次性冷纤维蛋白质血症与系统性硬化症中更严重的微血管病的参与有关:从回顾性观察性研究中得出的结果

Gilda Sandri1,2,3, Gabriele Amati4,5, Amelia Spinella4

  • 1Rheumatology Unit, Scleroderma Unit, University Hospital of Modena, Via del Pozzo, 71-41125, Modena, Italy. gilda.sandri@unimore.it.

Clinical rheumatology
|January 20, 2025
PubMed
概括

结晶纤维素生成症在全身性硬化症 (SSc) 患者中很常见,并且与严重的微血管问题有关. 对冷纤维素 (CF) 的测试可以指导早期使用内甲素受体对抗剂 (ERA) 的治疗,以预防数字截肢和死亡等并发症.

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