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Li-Han Goh1, Madhavan Manoharan2, Khean-Lee Goh3

  • 1Faculty of Medicine, St Vincent's Clinical School The University of New South Wales Sydney New South Wales Australia.

概括

初级肠道淋巴管切除症 (PIL) 是一种罕见的疾病,导致蛋白质损失. 诊断需要肠道活检,治疗需要改变饮食以获得临床改善.