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Updated: May 4, 2026

Optimized LC-MS/MS Method for the High-throughput Analysis of Clinical Samples of Ivacaftor, Its Major Metabolites, and Lumacaftor in Biological Fluids of Cystic Fibrosis Patients
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在患有1型原发性高氧化尿症的儿科患者中,对卢马西兰的治疗反应可变

Sina Saffe1, Katja Doerry2, Anja K Büscher3

  • 1Department of Pediatrics, Asklepios Klinik Nord Heidberg, Hamburg, Germany.

Pediatric nephrology (Berlin, Germany)
|January 27, 2025
PubMed
概括

对1型原发性高氧化尿症 (PH 1) 的卢马西兰治疗显示出不同的结果,在许多但不是所有患者中降低了氧化酸盐水平. 定期监测对于评估长期疗效和结果至关重要.

关键词:
功能 功能 功能结石 结石是指结石的出现.脏结症是什么 脏结症氧沙酸盐是一种氧化酸盐.这是一种RNA干扰.

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