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Updated: May 28, 2025

Real-Time Fluorescent Measurement of Synaptic Functions in Models of Amyotrophic Lateral Sclerosis
08:59

Real-Time Fluorescent Measurement of Synaptic Functions in Models of Amyotrophic Lateral Sclerosis

Published on: July 16, 2021

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聚胺代谢失调有助于肌肉纤维在ALS的脆弱性

Veronica Ruggieri1, Silvia Scaricamazza2, Andrea Bracaglia1

  • 1Department of Anatomical, Histological, Forensic Sciences and Orthopedics, Sapienza University of Rome, 00161 Rome, Italy; Laboratory affiliated with Istituto Pasteur Italia-Fondazione Cenci Bolognetti, 00161 Rome, Italy.

Cell reports
|February 11, 2025
PubMed
概括

研究人员发现,聚胺的新陈代谢在骨肌肉中被破坏,在肌肉增生侧面硬化症 (ALS) 期间. 恢复这种途径改善了ALS小鼠模型中的肌肉功能,为治疗提供了新的可能性.

关键词:
CP:新陈代谢过程中的新陈代谢.科普:神经科学是什么意思骨髓缩侧面硬化症 (ALS) 是一种肌肉缩 肌肉缩 肌肉缩神经肌肉结节是一个神经肌肉结节.聚氨酸是多氨基的这是骨肌肉的骨架肌肉.空间转录学 空间转录学

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In Vivo Electrophysiological Measurement of Compound Muscle Action Potential from the Forelimbs in Mouse Models of Motor Neuron Degeneration06:35

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