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酸盐激酶的功能与红细胞特性和状细胞疾病的临床表现相关

M J M Traets1, J F Bos1, S van der Veen2

  • 1Department of Central Diagnostic Laboratory-Research, University Medical Center Utrecht, Utrecht University, Utrecht, the Netherlands.

American journal of hematology
|February 21, 2025
PubMed
概括

在状细胞病 (SCD) 红细胞 (RBC) 中,受损的酸盐激酶 (PK) 功能与疾病的严重程度有关. 较低的PK活性和稳定性与较差的红细胞功能和增加的临床并发症相关,表明PK激活治疗的潜力.

关键词:
酸激酶是一种酸激酶.红细胞代谢 红细胞代谢状细胞疾病是一种状细胞疾病.

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