在囊性纤维化中,儿童肺部恶化病的流行病学正在发生变化

Yaron Fireizen1, Mohamoud Ahmed2, Timothy Vigers3,4

  • 1Department of Pediatrics, Rady Children's Hospital, University of California San Diego, San Diego, California, USA.

Pediatric pulmonology
|February 28, 2025
PubMed
概括

在引入elexacaftor/tezacaftor/ivacaftor (ETI) 治疗后,因囊性纤维化 (CF) 肺部恶化而住院的病例显著减少. 该研究观察到患者人口统计和微生物学的变化,表明治疗格局的变化和持续的健康差异.

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