在儿童中罕见的复发性埃索诺菲尔囊炎的呈现
Yara Hazem Zaky1, Anas Fangelnor1, Mohammad I Bader1
1Paediatric Surgery, John Radcliffe Hospital, Oxford, UK.
BMJ case reports
|March 7, 2025
概括
乙性囊炎 (EC) 是一种罕见的儿科膀疾病,可以模仿恶性瘤. 这一案例突出了使用口服类固醇的青少年男性中复发性EC的成功管理.
科学领域:
- 儿科泌尿外科 儿科泌尿外科
- 尿瘤学 尿瘤学
背景情况:
- 乙性囊炎 (EC) 是一种罕见的儿科膀疾病.
- 它经常呈现出血和下泌尿道症状 (LUTS).
- 诊断EC可能具有挑战性,有时模仿膀恶性瘤.
研究的目的:
- 报告一个早期青少年男性患有eosinophilic囊炎的病例.
- 为了说明复发性EC的诊断挑战和管理.
- 突出口服类固醇在治疗复发性EC中的作用.
主要方法:
- 一个青少年男性的病例介绍,最初的症状是失尿和出血症.
- 诊断工作包括超声波,MRI,囊镜和活检.
- 管理涉及观察,后来,口服类固醇治疗复发.
主要成果:
- 最初的调查引起了由于膀壁损伤的恶性瘤的怀疑.
- 活检证实了埃索诺菲尔性囊炎 (EC).
- 患者经历了EC的复发三年后,成功地管理了口服类固醇.
结论:
- 在儿童和青少年中,异性囊炎可以呈现异常.
- 复发是可能的,需要持续监测.
- 口服类固醇可以作为治疗儿科EC复发的有效方法.
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