阿尔巴尼亚的视网母细胞瘤:一个25年的回顾分析
Enkeleda Duka1, Eduart Hashorva2, Mirzana Kapllanaj1
1Pediatric Hemato Oncology Service, UHC Mother Teresa, Tirana, Albania.
Turkish archives of pediatrics
|March 17, 2025
概括
这项研究介绍了阿尔巴尼亚第一个视网母细胞瘤 (RB) 病例系列,揭示了儿童的晚期诊断和晚期疾病. 早期检测计划对于改善这种服务不足的人群的结果至关重要.
科学领域:
- 眼科医生 眼科 眼科
- 儿科瘤学 儿科瘤学
- 全球健康 全球健康
背景情况:
- 视网母细胞瘤 (RB) 是全球最常见的眼内癌症.
- 没有先前关于阿尔巴尼亚RB的报道.
- 本研究通过介绍阿尔巴尼亚的第一个案例系列来弥补这一差距.
研究的目的:
- 描述阿尔巴尼亚视网膜母细胞瘤患者的表现,治疗和结果.
- 突出在低资源环境下诊断和治疗RB的挑战和需求.
主要方法:
- 对1998年至2023年间诊断的22名RB患者的回顾性病例系列分析.
- 来自阿尔巴尼亚特蕾莎修女大学医院中心临床图表的数据.阿尔巴尼亚.
- 分析包括流行病学,临床和治疗数据.
主要成果:
- 22名患者的诊断年龄超过25岁; 59%是女性,平均年龄为21.8个月.
- 41%的人有双边RB;18%的人有家族病史.
- 常见的症状包括白血病 (27%) 和 (14%);诊断往往延迟.
- 治疗主要包括核切除和化疗;许多患者在国外寻求治疗.
结论:
- 这是阿尔巴尼亚儿科视网膜母细胞瘤患者的第一个队列.
- 诊断时的晚期疾病强调了需要改进诊断和治疗资源的需要.
- 实施国家儿科查计划对于早期检测和更好的结果至关重要.
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