双侧乳头在一个患有脊髓膜膜瘤的儿童:一个案例报告
Qi-Yuan Song1, Kui Lv1, Tian-Yi Luo2
1Department of Ophthalmology, Shenzhen Children's Hospital, Shenzhen, Guangdong, China.
The American journal of case reports
|March 20, 2025
概括
儿童的双边 papilledema 可能表明脊髓瘤,如myxopapillary ependymoma. 早期脊柱MRI和神经评估对于诊断和改善结果至关重要.
科学领域:
- 神经学 神经学
- 眼科医生 眼科 眼科
- 儿科瘤学 儿科瘤学
背景情况:
- 肌皮层上瘤是一种罕见的儿科脊柱瘤,通常会影响脊柱的下部.
- 眼部并发症不常见,但可能发生,呈现为双边 papilledema.
- 这一案例凸显了在患有视力障碍和神经症状的儿科患者中考虑脊髓瘤的重要性.
研究的目的:
- 报告小儿病患出现双侧 papilledema 的 myxopapillary ependymoma 的病例.
- 强调诊断挑战和脊柱MRI在这种情况下的重要性.
- 要强调眼科医生需要在差异诊断中考虑脊髓瘤的必要性.
主要方法:
- 一个12岁男孩的病例报告,患有复发的视力丧失和脊柱疼痛.
- 眼科检查显示双边 papilledema. 在眼科检查显示双边 papilledema.
- 腰部刺穿显示脑脊髓液压力和蛋白质升高.
- 脊柱MRI识别一个占用空间的病变.
- 神经外科干预和组织病理学证实了世卫组织2级的myxopapillary ependymoma.
主要成果:
- 该患者出现了双边乳头发疹,神经症状,以及CSF压力/蛋白质升高.
- 脊柱MRI证实了内损伤,诊断为myxopapillary膜瘤.
- 手术切除导致最初的视觉改善和神经恢复.
- 瘤复发需要三个月后进行第二次手术.
结论:
- 眼部并发症,如 papilledema,是罕见的,但重要的指标的儿科myxopapillary尾瘤.
- 迅速的眼科识别症状和全面的神经评估至关重要.
- 早期脊柱MRI对于防止误诊和确保及时干预以获得更好的患者结果至关重要.
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