右侧部分异常的肺静脉连接与完整的心房隔膜和小左心室:在右转心脏中
Sandeep Chakraborty1, Bharath Veerabhadraiah1, Mayank Yadav1
1Department of Cardiothoracic and Vascular Surgery, All India Institute of Medical Sciences, New Delhi, 10029 India.
Indian journal of thoracic and cardiovascular surgery
|March 27, 2025
概括
这项研究详细介绍了一种罕见的部分异常肺静脉连接的罕见病例,其中心脏隔膜完好,左心脏小心脏和冠状动脉鼻扩张. 手术纠正是成功的,患者康复良好.
科学领域:
- 心脏病学 心脏病学
- 遗传性心脏病是一种先天性心脏病.
- 心脏外科手术 心脏外科手术
背景情况:
- 部分异常肺静脉连接 (PAPVC) 是一种罕见的先天性心脏缺陷 (CHD),影响0.4-0.7%的人口.
- 带有完整的心房隔膜 (IAS) 的PAPVC非常罕见.
- 小左心室 (LA) 和扩大冠状动脉鼻 (CS) 的相关发现甚至更罕见.
研究的目的:
- 报告一个罕见的孤立右侧PAPVC病例,其中包括IAS,双边SVC,扩张的CS,以及右转心脏中的小LA.
- 描述这种复杂异常的手术管理和结果.
主要方法:
- 通过中枢椎切除术进行了PAPVC的手术纠正.
- 该程序涉及PAPVC重定向和LA增强,使用双心附属体方法.
主要成果:
- 该患者呈现出心脏异常的独特组合,包括右侧PAPVC到RA,双边SVC,IAS,扩张的CS和小LA.
- 手术干预是成功的,没有并发症.
- 患者表现出无事件的恢复,并在1个月的随访中表现良好.
结论:
- 这一案例凸显了识别和手术治疗PAPVC罕见变体的重要性.
- 即使在复杂的表现中,也可以成功地进行手术纠正,从而导致患者的良好结果.
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