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Updated: May 17, 2025

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ATP含量可以告诉我们什么关于巴斯综合征肌肉表型?

Jeffrey J Brault1, Simon J Conway2

  • 1Department of Anatomy, Cell Biology & Physiology, Indiana University School of Medicine, Indianapolis, IN 46202, USA.

Journal of translational genetics and genomics
|March 31, 2025
PubMed
概括

巴斯综合征 (BTHS) 涉及由于TAFAZZIN突变导致的能量赤字. 本综述探讨了BTHS中条纹肌肉的能量,重点关注线粒体ATP的产生及其对肌肉功能的影响.

关键词:
巴斯综合征是什么意思 巴斯综合征是什么意思塔法扎辛 (TAFAZZIN) 是一个古老的宗教.腺三酸盐是什么?卡尔迪奥利平因 (cardiolipin) 是一种心脏质蛋白质.能源学 能源学 能源学线粒体中的线粒体.有条纹的肌肉肌肉.

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