Hayley J Duxbury1, Vincent W Lee2,3, Fiona Kwok4

  • 1Tissue Pathology and Diagnostic Oncology, Institute of Clinical Pathology and Medical Research, Westmead Hospital, Westmead, New South Wales, Australia.

BMJ case reports
|April 3, 2025
PubMed
概括

这项研究详细介绍了一种罕见的增殖性血球炎病例,其中单克隆性免疫球蛋白沉积与血栓性微血管病变 (TMA) 同时发生. 用博特佐米布治疗和血交换在患者中实现了长期的临床稳定.