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Updated: May 8, 2025

Investigating von Willebrand Factor Pathophysiology Using a Flow Chamber Model of von Willebrand Factor-platelet String Formation
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Investigating von Willebrand Factor Pathophysiology Using a Flow Chamber Model of von Willebrand Factor-platelet String Formation

Published on: August 14, 2017

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临床表型和病理生理机制是潜在的定性低VWF

Ferdows Atiq1, Robin Blok2, Calvin van Kwawegen3

  • 1Erasmus MC, Netherlands.

Blood
|April 25, 2025
PubMed
概括

·维勒布兰德因子 (VWF) 活性中的轻度功能缺陷,称为低VWF-QL,是常见的,并导致显著的出血. 与2型VWD相比,这些患者具有明显的临床特征.

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